Journal of Clinical Images and Medical Case Reports
ISSN 2766-7820
Clinical Image - Open Access, Volume 5
Zinner syndrome in pediatric age: Clinical image
Francisca Galhardo Saraiva1*; Carolina Oliveira Gonçalves1; Vanda Bento1,2; Isabel França3
1Department of Children and Young People, Pediatrics Service, Portugal.
2Department of Children and Young People, Nephrology Consultation, Hospital Prof. Dr. Fernando Fonseca, Portugal.
3Department of Children and Young People, Pediatric Surgery Consultation, Hospital Prof. Dr. Fernando Fonseca, Portugal.
*Corresponding Author : Francisca Galhardo S
Department of Children and Young People, Pediatrics Service, Portugal.
Email: [email protected]
Received : Jan 11, 2024
Accepted : Jan 30, 2024
Published : Feb 06, 2024
Archived : www.jcimcr.org
Copyright : © Saraiva FG (2024).
Abstract
Zinner Syndrome (ZS) is a rare genitourinary malformation characterized by the triad of unilateral seminal vesicle cyst (QVS), ipsilateral Multicystic Displastic Kidney (MCDK), and obstruction of the ejaculatory duct. This condition is rare in pediatric age and both diagnosis and treatment are challenging.
Citation: Saraiva FG, Gonçalves CO, Bento V, França I. Zinner syndrome in pediatric age: Clinical image. J Clin Images Med Case Rep. 2024; 5(2): 2840.
Case presentation
We present a case of a child with a prenatal diagnosis of leftsided MCDK which was confirmed by postnatal ultrasound. At the age of 10, during a follow-up ultrasound, a cystic formation was identified in association with the left seminal vesicle, raising the diagnostic of ZS. Currently, the patient remains asymptomatic and is undergoing regular clinical and imaging surveillance.
Conclusion
In conclusion, ZS is rare in pediatric age. However, it should be considered in the differential diagnosis of cystic masses within the pelvis in males with ipsilateral renal anomalies. A conservative treatment with a long-term follow-up is a safe option in the management of asymptomatic or poorly symptomatic patients, thus reserving the surgical approach only in cases with symptoms.